Myxoma Of The Mitral Annulus

Abstract

SUMMARY: A case of “Syndrome” cardiac myxoma involving the mitral annulus is reported. The correct preoperative diagnosis of this exceedingly rare site was established using two-dimensional echocardiography. The superiority of this simple atraumatic investigation over conventional angiocardiography for diagnosis of atrial myxomas is discussed. DISCUSSION: ‘Sporadic’ atrial myxomas are typically solitary and pedunculated whereas ‘Syndrome’ cardiac myxomas are characterised by presentation in young age, atypical tumour site, skin freckles, benign endocrine neoplasms, familial tendency and a high rate of tumour recurrence (1821%).Hence, the changing scene of surgical management of ‘syndrome’ cardiac myxoma speaks of the necessity of correct localisation of tumour site prior to surgical intervention.