ARRHYTHMOGENIC RIGHT VENTRICULAR DYSPLASIA - CASE REPORT FROM PAKISTAN AND REVIEW OF LITERATURE

Abstract

Arrhythmogenic right ventricular dysplasia (ARVD) is disorder of cardiac muscle characterized by the replacement of myocytes by fibrofatty tissue and extracellular matrix.ARVD is a genetic cardiomyopathy characterized by fibrous-adipose substitution of the right (6) and rarely of the left ventricular myocardium (7).An important focus of the evaluation of a patient diagnosed with ARVD is to identify those at risk for SCD.ARVD is a rare disorder with a very heterogenous presentation. The disease is frequently asymptomatic until adolescence and the findings on testing are subtle - hence frequently missed.