VERTICAL PDA STENTING IN PULMONARY ATRESIA WITH INTACT INTERVENTRICULAR SEPTUM

Abstract

ABSTRACT Pulmonary atresia with intact interventricular septum(PA-IVS) is a rare congenital lesion. PA-IVS involves complete blockage of the pulmonary valve located on the right side of the heart. This blockage thus prevents the flow of blood to the lungs. Because of this lack of blood flowing through the right side of the heart, the structures on that side, such as the pulmonary valve and the tricuspid valve, may be abnormally small. The genetic cause of PA-IVS is unknown. We report a 6- month-old infant with congenital heart disease including; pulmonary atresia, intact ventricular septum, right ventricular hypoplasia, and vertical persistant ductus arteriosus (PDA) arising from left subclavian artery with stenosis at pulmonary end. PDA stenting was performed with successful hemodynamic after procedure.